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GAA (NM_001079803) Human Mass Spec Standard
CAT＃: PH315840
GAA MS Standard C13 and N15-labeled recombinant protein (NP_001073271)
View other "GAA" proteins (12)
|
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CNY 19,520.00
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Specifications
| Product Data | |
| Description | GAA MS Standard C13 and N15-labeled recombinant protein (NP_001073271) |
| Species | Human |
| Expression Host | HEK293 |
| Expression cDNA Clone or AA Sequence | RC215840 |
| Predicted MW | 105.3 kDa |
| Protein Sequence |
>RC215840 protein sequence
Red=Cloning site Green=Tags(s) MGVRHPPCSHRLLAVCALVSLATAALLGHILLHDFLLVPRELSGSSPVLEETHPAHQQGASRPGPRDAQA HPGRPRAVPTQCDVPPNSRFDCAPDKAITQEQCEARGCCYIPAKQGLQGAQMGQPWCFFPPSYPSYKLEN LSSSEMGYTATLTRTTPTFFPKDILTLRLDVMMETENRLHFTIKDPANRRYEVPLETPHVHSRAPSPLYS VEFSEEPFGVIVRRQLDGRVLLNTTVAPLFFADQFLQLSTSLPSQYITGLAEHLSPLMLSTSWTRITLWN RDLAPTPGANLYGSHPFYLALEDGGSAHGVFLLNSNAMDVVLQPSPALSWRSTGGILDVYIFLGPEPKSV VQQYLDVVGYPFMPPYWGLGFHLCRWGYSSTAITRQVVENMTRAHFPLDVQWNDLDYMDSRRDFTFNKDG FRDFPAMVQELHQGGRRYMMIVDPAISSSGPAGSYRPYDEGLRRGVFITNETGQPLIGKVWPGSTAFPDF TNPTALAWWEDMVAEFHDQVPFDGMWIDMNEPSNFIRGSEDGCPNNELENPPYVPGVVGGTLQAATICAS SHQFLSTHYNLHNLYGLTEAIASHRALVKARGTRPFVISRSTFAGHGRYAGHWTGDVWSSWEQLASSVPE ILQFNLLGVPLVGADVCGFLGNTSEELCVRWTQLGAFYPFMRNHNSLLSLPQEPYSFSEPAQQAMRKALT LRYALLPHLYTLFHQAHVAGETVARPLFLEFPKDSSTWTVDHQLLWGEALLITPVLQAGKAEVTGYFPLG TWYDLQTVPVEALGSLPPPPAAPREPAIHSEGQWVTLPAPLDTINVHLRAGYIIPLQGPGLTTTESRQQP MALAVALTKGGEARGELFWDDGESLEVLERGAYTQVIFLARNNTIVNELVRVTSEGAGLQLQKVTVLGVA TAPQQVLSNGVPVSNFTYSPDTKVLDICVSLLMGEQFLVSWC TRTRPLEQKLISEEDLAANDILDYKDDDDKV |
| Tag | C-Myc/DDK |
| Purity | > 80% as determined by SDS-PAGE and Coomassie blue staining |
| Concentration | >0.05 µg/µL as determined by microplate BCA method |
| Labeling Method | Labeled with [U- 13C6, 15N4]-L-Arginine and [U- 13C6, 15N2]-L-Lysine |
| Buffer | 25 mM Tris-HCl, 100 mM glycine, pH 7.3 |
| Reference Data | |
| RefSeq | NP_001073271 |
| RefSeq Size | 3597 |
| RefSeq ORF | 2856 |
| Synonyms | LYAG |
| Locus ID | 2548 |
| Cytogenetics | 17q25.3 |
| Summary | This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2016] |
| Protein Families | Druggable Genome, Transmembrane |
| Protein Pathways | Galactose metabolism, Lysosome, Metabolic pathways, Starch and sucrose metabolism |
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| 蛋白相关资源 |
Other Versions
| SKU | Description | Size | Price |
|---|---|---|---|
| LC400052 | GAA HEK293T cell transient overexpression lysate (as WB positive control) |
CNY 900.00 |
|
| LC421540 | GAA HEK293T cell transient overexpression lysate (as WB positive control) |
CNY 1,470.00 |
|
| LC421541 | GAA HEK293T cell transient overexpression lysate (as WB positive control) |
CNY 900.00 |
|
| LY400052 | Transient overexpression lysate of glucosidase, alpha; acid (GAA), transcript variant 1 |
CNY 3,080.00 |
|
| LY421540 | Transient overexpression lysate of glucosidase, alpha; acid (GAA), transcript variant 2 |
CNY 4,840.00 |
|
| LY421541 | Transient overexpression lysate of glucosidase, alpha; acid (GAA), transcript variant 3 |
CNY 3,080.00 |
|
| PH308033 | GAA MS Standard C13 and N15-labeled recombinant protein (NP_001073272) |
CNY 19,520.00 |
|
| PH315796 | GAA MS Standard C13 and N15-labeled recombinant protein (NP_000143) |
CNY 19,520.00 |
|
| TP308033 | Recombinant protein of human glucosidase, alpha; acid (GAA), transcript variant 3, 20 µg |
CNY 2,900.00 |
|
| TP315796 | Recombinant protein of human glucosidase, alpha; acid (GAA), transcript variant 1, 20 µg |
CNY 2,900.00 |
|
| TP315840 | Recombinant protein of human glucosidase, alpha; acid (GAA), transcript variant 2, 20 µg |
CNY 2,900.00 |
|
| TP701073 | Purified recombinant protein of Human glucosidase, alpha, acid (GAA), with N-terminal His tag, secretory expressed in HEK293 cells, 20ug |
CNY 7,106.00 |
