PEX5 (NM_000319) Human 3' UTR Clone
CAT#: SC213651
3' UTR clone of peroxisomal biogenesis factor 5 (PEX5) transcript variant 2 for miRNA target validation
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CNY 4,845.00
货期*
3周
规格
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经常一起买 (2)
Specifications
Product Data | |
Product Name | PEX5 (NM_000319) Human 3' UTR Clone |
Vector | pMirTarget |
Synonyms | PBD2A; PBD2B; PTS1-BP; PTS1R; PXR1; RCDP5 |
ACCN | NM_000319 |
Insert Size | 1266 bp |
Sequence Data |
>SC213651 3’UTR clone of NM_000319
The sequence shown below is from the reference sequence of NM_000319. The complete sequence of this clone may contain minor differences, such as SNPs. Blue=Stop Codon Red=Cloning site GGCAAGTTGGACGCCCGCAAGATCCGCGAGATTCTCATTAAGGCCAAGAAGGGCGGAAAGATCGCCGTG TAACAATTGGCAGAGCTCAGAATTCAAGCGATCGCC CTCCTAACTATGTTTGGCCTGCCCCAGTGACAGTGGGACGGGCTGCCCTGTGAGTGTCCACCTGGAGGG ATCCCCGCTTTGGATGTGATTCCCTCTCCCCAAATGGGCCTACCAAGGGGGCGGGCTGATGACCATAAG CGGTACGGCCTTTCAGGAGCTGCCTCAACGTAGGGGTGGGTAGTCTGTGTTCTAGTTCCTACATAATTG TAGGAAAATGAGCTGTGTCATCTCTGAGTCCCTTGGTAATTCAAGGGCTGTACATCCAGCTACAGATCT CTCTGCTCATCATGCCCTTTCTTGGTGCTGCTTTTTGGGTAGGACCCCACGATTTAGGGTAACTGTTAT CATCAGCTGCCATTTCTGATAGGGTCTACCACATCTGTAATGTCTGTCCTTTCCCCCACTTTTACTGGG AATTGATAGTCCAGCTTCCTTGGGCAGTGTAAGTAGGAGGTTCATCTGCTGTGCGCCTCTAATGTCTGT CTGGATGGGATGTGTTAGGAGTTGGCCTGTTGGGTTGAATTGTTGATTTGGCTGAGCAGAGCTGAGTTT TGGTAGGAGTGCTCATGGTTCTGTCATTCTTGGACCTCTCCTGGCTGAGCTCTGATTCCCTGTGAGCAC GATGCTGATGCAATAGTCCTGTGTCATCACTGCAGCGGTCCTCAGGAGCTGCCAGGGCCAATTGCTACA GAGTGTCTGGGTGTGTGGCATAGGAGGAAGGTTTGCTTGTGAAATGAGGCTGGGTGGGAGCGGGGAGGG ACTAGATCAGAAGAGATCAAGGGCTCTATTCAGGAACGTTGGTGGGAGGACAGAGCAAGTGGGAAGGGG GTATGGTGAGTGCGGCAATCCCTCATCCTCTTAGAAGCACCTGTGAATGGGAATTGAGCCAACTGTTAT AGAAAATTGGTTCAGAAAGTGCAATCTTGCCAGATTTCTAGCAAATAGGTTCAGTGTTACCATAAGCCT TTGCTGTACTTCTTGAAATGTTTCTAGGGGAGAGCATTGGAAAATCCCCTTCCCCCATCTAGATCGAAG GAAGATGAGGGAGCAGCTTGGATTCTTCTCAGTTGTCCCCTGCATGGGGAGATACACTAACCCCCAGAA ATGACTGCTAAGCCTCTTGCCTTGTCTTTAGTAGCTAATGATCAGAGAGATTTTTTTTTTAAACTACCA TGGTCCCAGGATTCCATCCTGAAATTTATTTTTCTTTGTATGAATATGTGTAAATGATTTAAAAATAAA ACTGTAAAATATTTGTACGAAGAA ACGCGTAAGCGGCCGCGGCATCTAGATTCGAAGAAAATGACCGACCAAGCGACGCCCAACCTGCCATCA CGAGATTTCGATTCCACCGCCGCCTTCTATGAAAGG |
Restriction Sites | SgfI-MluI |
OTI Disclaimer | Our molecular clone sequence data has been matched to the sequence identifier above as a point of reference. Note that the complete sequence of this clone is largely the same as the reference sequence but may contain minor differences , e.g., single nucleotide polymorphisms (SNPs). |
Reference Data | |
RefSeq | NM_000319.5 |
Synonyms | PBD2A; PBD2B; PTS1-BP; PTS1R; PXR1; RCDP5 |
Summary | The product of this gene binds to the C-terminal PTS1-type tripeptide peroxisomal targeting signal (SKL-type) and plays an essential role in peroxisomal protein import. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of neonatal adrenoleukodystrophy (NALD), a cause of Zellweger syndrome (ZWS) as well as may be a cause of infantile Refsum disease (IRD). Alternatively spliced transcript variants encoding different isoforms have been identified. [provided by RefSeq, Oct 2008] |
Locus ID | 5830 |
MW | 47.3 |
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