FKRP (NM_024301) Human Untagged Clone
CAT#: SC112266
FKRP (untagged)-Human fukutin related protein (FKRP), transcript variant 1
CNY 3,656.00
Product images
Specifications
Product Data | |
Type | Human Untagged Clone |
Tag | Tag Free |
Synonyms | FKTR; LGMD2I; LGMDR9; MDC1C; MDDGA5; MDDGB5; MDDGC5 |
Vector | pCMV6-XL6 |
E. coli Selection | Ampicillin (100 ug/mL) |
Mammalian Cell Selection | None |
Sequence Data |
>NCBI ORF sequence for NM_024301, the custom clone sequence may differ by one or more nucleotides
ATGCGGCTCACCCGCTGCCAGGCTGCCCTGGCGGCCGCCATCACCCTCAACCTTCTGGTCCTCTTCTATG TCTCGTGGCTGCAGCACCAGCCTAGGAATTCCCGGGCCCGGGGGCCCCGTCGTGCCTCTGCTGCCGGCCC CCGTGTCACCGTCCTGGTGCGGGAGTTCGAGGCATTTGACAACGCGGTGCCCGAGCTGGTAGACTCCTTC CTGCAGCAAGACCCAGCCCAGCCCGTGGTGGTGGCAGCCGACACGCTCCCCTACCCGCCCCTGGCCCTGC CCCGCATCCCCAACGTGCGTCTGGCGCTGCTCCAGCCCGCCCTGGACCGGCCAGCCGCAGCCTCGCGCCC GGAGACCTACGTGGCCACCGAGTTTGTGGCCCTAGTACCTGATGGGGCGCGGGCTGAGGCACCTGGCCTG CTGGAGCGCATGGTGGAGGCGCTCCGCGCAGGAAGCGCACGTCTGGTGGCCGCCCCGGTTGCCACGGCCA ACCCTGCCAGGTGCCTGGCCCTGAACGTCAGCCTGCGAGAGTGGACCGCCCGCTATGGCGCAGCCCCCGC CGCGCCCCGCTGCGACGCCCTGGACGGAGATGCTGTGGTGCTCCTGCGCGCCCGCGACCTCTTCAACCTC TCGGCGCCCCTGGCCCGGCCGGTGGGCACCAGCCTCTTTCTGCAGACCGCCCTTCGCGGCTGGGCGGTGC AGCTGCTGGACTTGACCTTCGCCGCGGCGCGCCAGCCCCCGCTGGCCACGGCCCACGCGCGCTGGAAGGC TGAGCGCGAGGGACGCGCTCGGCGGGCGGCGCTGCTCCGCGCGCTGGGCATCCGCCTAGTGAGCTGGGAA GGCGGGCGGCTGGAGTGGTTCGGCTGCAACAAGGAGACCACGCGCTGCTTCGGAACCGTGGTGGGCGACA CGCCCGCCTACCTCTACGAGGAGCGCTGGACGCCCCCCTGCTGCCTGCGCGCGCTGCGCGAGACCGCCCG CTATGTGGTGGGCGTGCTGGAGGCTGCGGGCGTGCGCTACTGGCTCGAGGGCGGCTCACTGCTGGGGGCC GCCCGCCACGGGGACATCATCCCATGGGACTACGACGTGGACCTGGGCATCTACTTGGAGGACGTGGGCA ACTGCGAGCAGCTGCGGGGGGCAGAGGCCGGCTCGGTGGTGGATGAGCGCGGCTTCGTATGGGAGAAGGC GGTCGAGGGCGACTTTTTCCGCGTGCAGTACAGCGAAAGCAACCACTTGCACGTGGACCTGTGGCCCTTC TACCCCCGCAATGGCGTCATGACCAAGGACACGTGGCTGGACCACCGGCAGGATGTGGAGTTTCCCGAGC ACTTCCTGCAGCCGCTGGTGCCCCTGCCCTTTGCCGGCTTCGTGGCGCAGGCGCCTAACAACTACCGCCG CTTCCTGGAGCTCAAGTTCGGGCCCGGGGTCATCGAGAACCCCCAGTACCCCAACCCGGCACTGCTGAGT CTGACGGGAAGCGGCTGA >OriGene 5' read for NM_024301 unedited
NNGGTCCTTACCCCCGCCCCGTTGNCGCAAAGGGCGGTAGGCGTGTACGGTGGGAGGTCT ATATAAGCAGAGCTCATTTAGGTGACACTATAGAATACAAGCTACTTGTTCTTTTTGCAG CGGCCGCGAATTCGGCACGAGGCTTCGGCCCCATGCGGCTCACCCGCTGCCAGGCTGCCC TGGCGGCCGCCATCACCCTCAACCTTCTGGTCCTCTTCTATGTCTCGTGGCTGCAGCACC AGCCTAGGAATTCCCGGGCCCGGGGGCCCCGTCGTGCCTCTGCTGCCGGCCCCCGTGTCA CCGTCCTGGTGCGGGAGTTCGAGGCATTTGACAACGCGGTGCCCGAGCTGGTAGACTCCT TCCTGCAGCAAGACCCAGCCCAGCCCGTGGTGGTGGCAGCCGACACGCTCCCCTACCCGC CCCTGGCCCTGCCCCGCATCCCCAACGTGCGTCTGGCGCTGCTCCAGCCCGCCCTGGACC GGCCAGCCGCAGCCTCGCGCCCGGAGACCTACGTGGCCACCGAGTTTGTGGCCCTAGTAC CTGATGGGGCGCGGGCTGAGGCACCTGGCCTGCTGGAGCGCATGGTGGAGGCGCTCCGCG CAGGAAGCGCACGTCTGGTGGCCGCCCCGGTTGCCACGGCCAACCCTGCCAGGTGCCTGG CCCTGAACGTCAGCCTGCGAGAGTGGACCGCCCGCTATGGCGCAGCCCCCGCCGNGCCCC GCTGCGACGCCCTGGACGGAGATGCTGTGGTGCTCCTGCGCGCCCGCGACCTCTTAACCT CTCGGCGCCCCTGCCCGCCGGGGGCACCAGCCTCTTCTGCAGACGCCCTCGCGCTGGCCG TGCACCTGCTGACTTGACTTCCCCGGGNGCGCAGCCCCGTGGCCCGCCCACCCGCTGAAG GCTGACGCAGACCGCC >OriGene 3' read for NM_024301 unedited
NCCGTATACTATGNACCGCGCCGCATTCTANGATCGGTTTTTTTTTTTTTTTTTTTAAAA TGGAATAATTTAAGCTTTATTACTAACATACAGATAATAGTATCTGTATATATTTATAAA TAAATATACACATATTGGGAATACATGCCCAAATACCATTTATTCTTAGGTGCATAATCA AATAAGGAAGGCTGCCATTGCTTTCACCTGCTAAGTGGGTCTCCAAGCCCCTCTTGGGGA CCATGACTAGAGAGGGGCATAGTGGGTAAGACAATTGTGGGCTCCAGAGCCTGACCACCT GGGTTCAAGCCCCCGATCTGCCCCTTCCTAAGCTGCCTGACCTTGAGCAAGTGACTTCAC GATTCTGGCCTCAGCTTTTTCATCTGTGTAATGAAAATAATAGCAGCTGTCACTTCAAAG GGCTGAGGTGAGGGACGCATTAATTGATCCAGGTGAAACACTGAGAATGGTGCCTGGTAC CCAGTAAGTGCTCAGTGAGTGTGAGCTATGGTTATTGTCTACACTGCCGTGCAAGTGGGG AATTAGGTGCAGACAGCTGAAATAATGAGGTATTAGTCATGAGTGGAGCTGCGATTCAAA AATCGGGTCTTTTTCTTTTTTAAAAATAGAGACAGGGTCTTGGCATGTTGCCGAAGCTGG TCTCAGACTCCTGGGCTCAAACGATCCTCCCACCTCGGCCTCTCAAAATGCTGGGAGTAC ACGCGTGAGACCCCGCGCCCGGGCCAAAACCCGGTTTTTGACCACCAACCCCCCTCGGAG CTCTGAGCATTTTCTTCTCTGGAAGACGAAAAAAATTCTTTTCAATCTTGATATAACAAT TAAGAAAACATGCCGGGCACAGGGCTCTTCCAAGAAGG |
Restriction Sites | NotI-NotI |
ACCN | NM_024301 |
Insert Size | 3000 bp |
OTI Disclaimer | Our molecular clone sequence data has been matched to the reference identifier above as a point of reference. Note that the complete sequence of our molecular clones may differ from the sequence published for this corresponding reference, e.g., by representing an alternative RNA splicing form or single nucleotide polymorphism (SNP). |
Product Components | The ORF clone is ion-exchange column purified and shipped in a 2D barcoded Matrix tube containing 10ug of transfection-ready, dried plasmid DNA (reconstitute with 100 ul of water). |
Reconstitution | 1. Centrifuge at 5,000xg for 5min. 2. Carefully open the tube and add 100ul of sterile water to dissolve the DNA. 3. Close the tube and incubate for 10 minutes at room temperature. 4. Briefly vortex the tube and then do a quick spin (less than 5000xg) to concentrate the liquid at the bottom. 5. Store the suspended plasmid at -20°C. The DNA is stable for at least one year from date of shipping when stored at -20°C. |
Reference Data | |
RefSeq | NM_024301.2, NP_077277.1 |
RefSeq Size | 3422 bp |
RefSeq ORF | 1488 bp |
Locus ID | 79147 |
UniProt ID | Q9H9S5 |
Protein Families | Transmembrane |
Gene Summary | This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, cognitive disability, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq, Oct 2008] Transcript Variant: This variant (1) differs in the 5' UTR compared to variant 1. Variants 1 and 2 encode the same protein. |
Documents
Product Manuals |
FAQs |
SDS |
Resources
Other Versions
SKU | Description | Size | Price |
---|---|---|---|
RC200941 | FKRP (Myc-DDK-tagged)-Human fukutin related protein (FKRP), transcript variant 1 |
CNY 3,656.00 |
|
RC200941L1 | Lenti ORF clone of Human fukutin related protein (FKRP), transcript variant 1, Myc-DDK-tagged |
CNY 6,056.00 |
|
RC200941L2 | Lenti ORF clone of Human fukutin related protein (FKRP), transcript variant 1, mGFP tagged |
CNY 5,890.00 |
|
RC200941L3 | Lenti ORF clone of Human fukutin related protein (FKRP), transcript variant 1, Myc-DDK-tagged |
CNY 5,890.00 |
|
RC200941L4 | Lenti ORF clone of Human fukutin related protein (FKRP), transcript variant 1, mGFP tagged |
CNY 5,890.00 |
|
RG200941 | FKRP (tGFP-tagged) - Human fukutin related protein (FKRP), transcript variant 1 |
CNY 5,256.00 |